Modified cone procedure along with bidirectional cavopulmonary shunt for Ebstein anomaly in adult patients

Authors

  • Rakesh Sharma Department of Cardiothoracic Surgery, G. B. Pant Institute of Postgraduate Medical Education and Research (GIPMER), New Delhi, India
  • Satyajit Samal Department of Cardiothoracic Surgery, G. B. Pant Institute of Postgraduate Medical Education and Research (GIPMER), New Delhi, India
  • Rahul Banik Department of Cardiothoracic Surgery, G. B. Pant Institute of Postgraduate Medical Education and Research (GIPMER), New Delhi, India
  • Saket Aggarwal Department of Cardiothoracic Surgery, G. B. Pant Institute of Postgraduate Medical Education and Research (GIPMER), New Delhi, India
  • Sayyed Ehtesham Hussain Naqvi Department of Cardiothoracic Surgery, G. B. Pant Institute of Postgraduate Medical Education and Research (GIPMER), New Delhi, India
  • Mohammed Abid Geelani Department of Cardiothoracic Surgery, G. B. Pant Institute of Postgraduate Medical Education and Research (GIPMER), New Delhi, India

DOI:

https://doi.org/10.18203/2349-2902.isj20221825

Keywords:

Ebstein anomaly, Adult congenital heart disease, Modified cone reconstruction, Bidirectional cavopulmonary shunt, Tricuspid annuloplasty ring

Abstract

Ebstein anomaly is an uncommon congenital cardiac disease affecting the tricuspid valve and right ventricle. Da silva pioneered the cone reconstruction of tricuspid valve for surgical repair of this anomaly in 2007. We describe our experience of 5 adult patients who underwent cone repair along with a bidirectional cavopulmonary shunt and tricuspid annuloplasty ring placement at our institute. Five adult patients with Ebstein anomaly with progressive disease and symptoms were taken up cone reconstruction from 2019 to 2021. Along with cone reconstruction of tricuspid valve, we routinely added an end to side superior vena cava to right pulmonary artery shunt and a tricuspid annuloplasty ring in the newly formed tricuspid annulus in all cases. All patients tolerated the procedure well and easily weaned off cardiopulmonary bypass. There were no complications regarding bidirectional cavopulmonary shunt and only one patient had a temporary heart block which was managed conservatively. This series shows routine addition of a cavopulmonary shunt and an annuloplasty ring improves outcomes and can be performed at other experienced cardiac surgery centres.

 

Author Biography

Rakesh Sharma, Department of Cardiothoracic Surgery, G. B. Pant Institute of Postgraduate Medical Education and Research (GIPMER), New Delhi, India

MCH SENIOR RESIDENT , DEPARTMENT OG CARDIOTHORACIC SURGERY, GIPMER, NEW DELHI , INDIA

References

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Published

2022-07-26

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Case Series