DOI: http://dx.doi.org/10.18203/2349-2902.isj20214017

Acute intestinal obstruction in Peutz Jeghers syndrome: a case report

Gajendra Anuragi, Afroz I. Bagwan, Ramprakash V. S., Sugumar C., Naganath B. O. Lakshmanamoorthy

Abstract


Peutz Jeghers syndrome is an autosomal dominant hereditary disorder affecting male and female equally. It is characterised by mucocutaneous hyperpigmentation and hamartomatous polyp in gastrointestinal tract with increased risk of malignancy. We report here a case of 52-year-old patient with traits of Peutz jeghers syndrome presented with acute intestinal obstruction following colocolic intussusception. Peutz jeghers syndrome is an autosomal dominant inherited disorder. Individual may present in rare case with acute intestinal obstruction associated with intussusception due to polyps.


Keywords


Peutz Jeghers syndrome, Autosomal dominant, Malignancy, Intussusception

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References


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