A rare case report of aplasia cutis congenita of the scalp with triplet skin defects in non-syndromic newborn

Authors

  • Naim Sulaiman Abuzarifa Reconstructive Sciences Unit, Universiti Sains Malaysia (USM), Malaysia http://orcid.org/0000-0001-5929-3301
  • Wan Azman Wan Sulaiman Reconstructive Sciences Unit, Universiti Sains Malaysia (USM), Malaysia

DOI:

https://doi.org/10.18203/2349-2902.isj20210468

Keywords:

Aplasia cutis congenita, Triplet, Skin, Lesions

Abstract

Aplasia cutis congenita is an uncommon localized or widespread congenital skin condition characterized by the absence of the skin, and occasionally underlying tissues occurs in about one every 10.000 birth mostly in the scalp as single or more than one lesion and sometimes occurs in extremities and trunk with an uncertain cause and can be associated with numerous syndromes or can be sporadic which is diagnosed clinically and usually conservatively managed but sometimes surgical intervention needed. In this literature, we present nonsyndromic newborn Malay girl normally delivered with 35 weeks gestational age with triplet skin raw areas at the vertex of the scalp with well-demarcated defect round in shape measured about 0.5 in radius covered with a noninflammatory, necrotic patch. To our knowledge, many works of literatures presented Aplasia cutis congenita at the scalp with solitary single or occasionally more than one skin defect. In contrast, in our case, we present an infrequent rare case of triplet skin defect of aplasia cutis congenita for nonsyndromic newborns.

 

Author Biography

Naim Sulaiman Abuzarifa, Reconstructive Sciences Unit, Universiti Sains Malaysia (USM), Malaysia

Reconstructive Sciences Unit - Universiti Sains Malaysia (USM)

References

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Brzezinski P, Pinteala T, Chiriac AE, Foia L, Chiriac A. Aplasia cutis congenita of the scalp-what are the steps to be followed? Case report and review of the literature. Anais brasileiros de dermatologia. 2015;90(1):100-3.

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Adigun CG, Freeze ME, Wells MJ, Perry V, James WD. Aplasia cutis congenita. 2020. Available at: https://emedicine.medscape.com/article/1110134-overview. Accessed on 10 November 2020.

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Published

2021-02-25

Issue

Section

Case Reports