DOI: http://dx.doi.org/10.18203/2349-2902.isj20204703

Intestinal liposarcoma: an unusual cause for peritonitis

Siddartha Gowthaman, Ramanathan Manickam

Abstract


Liposarcoma is the commonest type of soft tissue sarcomas which can occur in any part of the body, most commonly involving the limbs and retroperitoneum but it rarely involves small bowel. Only very few cases had been reported of liposarcoma involving small intestine in the past. The clinical presentations of this type of tumour arising from small bowel are nonspecific mostly during the initial stages of the disease and because of this the disease is often diagnosed at advanced stage. We report a very rare case of primary small bowel liposarcoma of ileum which had spontaneously perforated leading to peritonitis in an elderly female who underwent laparotomy, the tumour mass is resected with adequate margins and primary bowel anastomosis was done. The patient was followed up for a year with no complication. Although the liposarcomas occurring in the gastrointestinal tract leading to intestinal perforation is extremely rare. This unique case represents an important learning point for all clinicians and pathologists.


Keywords


Liposarcoma, Atypical lipomatous tumor, Well-differentiated liposarcoma

Full Text:

PDF

References


Kransdorf MJ. Malignant soft-tissue tumours in a large referral population:distribution of diagnoses by age, sex and location. Am J Roentgenol. 1995;164:129-34.

De MM, Mangoni I, Gobatti D, Ghilardi G, Scorza R. Primary jejunal liposarcoma. Minerva gastroenterologica e dietologica. 2000;46(2):119-22.

Fletcher CDM, Unni KK, Mertens F: World Health Organization Classification of Tumors. Pathology and Genetics of Tumors of Soft Tissue and Bone. Int Agen Resea Canc. 2002.

Kooby DA, Antonescu CR, Brennan MF, Singer S. Atypical lipomatous tumor/well-differentiated liposarcoma of the extremity and trunk wall: importance of histological subtype with treatment recommendations. Ann Surg Oncol. 2004;11(1):78-84.

Kindblom LG, Angervall L, Svendsen P. Liposarcoma a clinicopathologic, radiographic and prognostic study. Acta Pathol Microbiol Scand Suppl. 1975:1-71.

Horiguchi H, Matsui M, Yamamoto T, Mochizuki R, Uematsu T, Fujiwara M, et al. A case of liposarcoma with peritonitis due to jejunal perforation. Sarco. 2003;7.

Benaragama KS, Neequaye SK, Maudgil D, Gordon AG. Small bowel liposarcoma-a rare cause of small bowel perforation. Cas Repo. 2010;2010:1020092364.

Sato T, Nishimura G, Nonomura A, et al. Intra-abdominal and retroperitoneal liposarcomas. Int Surg. 1999;84:163-7.