Presacral schwannoma: a bizarre presentation in the Pandora’s box of abdomen and pelvis

Authors

  • Harsha S. Poojary Department of General Surgery, A.J. Institute of Medical Sciences and Research Centre, Mangalore, Karnataka, India
  • Vishwanath Sherigar Department of Oncosurgery, A.J. Hospital and Research Centre, Mangalore, Karnataka, India
  • Abhinav Balaji Department of Urology, A.J. Hospital and Research Centre, Mangalore, Karnataka, India

DOI:

https://doi.org/10.18203/2349-2902.isj20202867

Keywords:

Presacral schwannoma, Ancient schwannoma, Antoni A, Antoni B, SMARCB1, LZTR1 mutation

Abstract

Schwannomas are benign tumors arising from the Schwann cells of nerve fibers. They are extremely rare in the pelvis accounting for only 1-3% of all schwannomas. These tumors are nonaggressive, slow growing, solitary neoplasms with an extremely low possibility of malignant transformation or recurrence after excision. We present a case of a 19 years old male with complaints of radiating pain from lower back to the left thigh associated with altered bowel and bladder habits. Following a detailed work up he underwent laparotomy and mass excision. Histopathological report revealed presacral schwannoma. Post-surgery patient improved symptomatically and is on regular follow up. There are a smaller number of cases of presacral schwannoma reported in the literature. Due to its outlandish striking presentation, diagnosis is very challenging. Although presacral schwannoma is rare, it should be considered as a differential diagnosis in the back of the mind of a surgeon while dealing a case of pelvic mass. In symptomatic and asymptomatic cases, surgical excision is the mainstay of treatment of these tumors.

Author Biographies

Harsha S. Poojary, Department of General Surgery, A.J. Institute of Medical Sciences and Research Centre, Mangalore, Karnataka, India

DEPARTMENT OF GENERAL SURGERY

JUNIOR RESIDENT (M.B.B.S, (M.S))

Vishwanath Sherigar, Department of Oncosurgery, A.J. Hospital and Research Centre, Mangalore, Karnataka, India

DEPARTMENT OF ONCOSURGERY

CONSULTANT ONCOSURGEON (M.B.B.S, M.S, MCH)

Abhinav Balaji, Department of Urology, A.J. Hospital and Research Centre, Mangalore, Karnataka, India

DEPARTMENT OF UROLOGY

SENIOR RESIDENT (M.B.B.S, MS GENERAL SURGERY, DNB GENERAL SURGERY, (MCH))

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Published

2020-06-25

Issue

Section

Case Reports