Clear cell sarcoma of kidney in an adult: an extremely rare case

Krishna Lanka, Karyampudi Bhramaramba, Venkata Ramana P, Padma Sunethri


Clear cell sarcoma of kidney is extremely rare in adults. It is a very malignant tumor, with a high tendency for relapse and a propensity for skeletal metastases, particularly skull. Treatment of clear cell sarcoma of kidney generally involves surgical intervention coupled with radiation and chemotherapy. This paper reports a case of adult clear cell sarcoma of kidney.


Clear cell sarcoma, Kidney, Renal tumors

Full Text:



Marsden HB, Lawler W, Kumar PM. Bone metastasizing renal tumor of childhood. Morphological and clinical features and differences from Wilms’ tumor. Cancer. 1978;42:1922-8.

Adanani A, Lalid R, Bouklata S, Ajana A, Hammani L, Imani F. Clear cell sarcoma of kidney in an adult: a case report. J Radiol. 2006;87:136-8.

Benchekroun A, Zannoud M, el Alj HA, Nouini Y, Marzouk M, Faik M. Clear cell sarcoma of the kidney: three case reports. Prog Urol. 2002;12(3):469-73.

Sotelo-Avila C, Gonzalez-Crussi F, Sadowinski S, Gooch WM III, Pena R. Clear cell sarcoma of the kidney. A clinicopathological study of 21 patients with long term follow-up evaluation. Hum Pathol. 1986;16:1219-30.

Amin MB, de Peralta-Venturina MN, Ro JY, El-Naggar A, Mackay B, Ordonez N. Clear cell sarcoma of kidney in an adolescent and in young adults; a report of four cases with ultrastructural, immunohistochemical, and DNA flow cytometric analysis. Am J Surg Pathol. 1999 Dec;23(12):1455-63.

Franco A, Dao TV, Lewis KN, Biddinger PW. A case of clear cell sarcoma of the kidney. Radiol Case. 2011;5(2):8-12.

Argani P, Beckwith BJ. Renal neoplasms of childhood. In: Mills, Stacey E, eds. Sternberg’s Diagnostic Surgical Pathology. 5th ed. Philadelphia: Lippincott Williams & Wilkins; 2010: 1819.