Jejunal atresia presenting as meconium cyst with polysplenia in a newborn: an extremely rare association

Authors

  • Rashi . Department of Paediatrics Surgery, All India Institute of Medical Sciences, Patna, Bihar, India
  • Kalyani Saha Basu Department of Paediatrics Surgery, Nil Ratan Sircar Medical College, Kolkata, India
  • Samiran Biswas Department of Paediatrics Surgery, B C Roy Post Graduate Institute of Paediatric Sciences, Kolkata, India
  • Shibsankar Barman Department of Paediatrics Surgery, Institute of Post Graduate Medical Education & Research, Kolkata, India

DOI:

https://doi.org/10.18203/2349-2902.isj20193366

Keywords:

Jejunal atresia, Polysplenia, Meconium cyst

Abstract

Jejunal atresia (JA) presenting as meconium cyst with polysplenia is an extremely rare condition. We reported a case presenting with abdominal distension and feculent vomiting. Exploration revealed a type IV JA with dilated proximal segment presented as a large cyst filled with air and meconium. Polysplenia diagnosed incidentally.

References

Komuro H, Amagai T, Hori T, Hirai M, Matoba K, Watanabe M et al. Placental vascular compromise in jejunoileal atresia. J Pediatr Surg. 2004;39(11):1701-5.

Rasool F, Mirza B. Polysplenia syndrome associated with situs inversus abdominus and type I jejunal atresia. APSP J Case Rep. 2011;2(2):18.

Asabe K, Yukitake K, Mori T, Mitsudome A, Shirakusa T. Biliary atresia associated with jejunal atresia and a review of the literature in Japan. Asian J Surg. 2005;28(2):154-7.

Grosfeld JA. Jejunoileal atresia and stenosis. In Pediatric Surgery 6th ed. Edited by: Grosfeld JL, O'Neill JA Jr, Fonkalsrud EW, Coran AG. Philadelphia:Mosby Elsevier; 2006:1269-88.

Barber GA, Whalen TV, Moore G: Polysplenia and Jejunal atresia with agenesis of the dorsal mesentery. J Pediatr Surg. 1989;24 (11):1161.

Ahmad S. Polysplenia Syndrome Associated With Heterotaxy of Abdominal Viscera and Type IV Intestinal Atresias. J Neonat Surg. 2012;1(3):45.

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Published

2019-07-25

Issue

Section

Case Reports