Rare case of retroperitoneal cystic lymphangioma in an adult

Cherring Tandup, Anish Chowdhury, Yashwant Raj Sakaray, Nasika Venkata Kanaka Naga Karthik


Cystic lymphangioma is benign tumor originating from the lymphatic vessels. Most commonly occurs in childhood and in the head or neck regions, retroperitoneal localization and presentations in adulthood are rare. Making a pre-operative diagnosis is challenging, and only possible subsequent to the histological examination. En bloc resection is the recommended treatment for cystic lymphangioma, and recurrence occurs due to an incomplete excision. We here present a case of 40 year female presenting with progressive palpable lump associated with pain in right quadrant of abdomen, which on computed tomography revealed a large retroperitoneal cystic lesion probably lymphanigoma or cystic mesothelioma.


Lymphangioma, Cyst, Retroperitoneal, Adult

Full Text:



Stavropoulos M, Vagianos C, Scopa CD, Dragotis C, Androulakis J. Solitary hepatic lymphangioma a rare benign tumour: a case report. HPB Surg. 1994;8:33–6.

Bertino G, Ardiri A, Demma S, GiuseppeCalvagno S, Toro A, Basile E, et al. Rare benign tumors of the liver: still rare? J Gastrointest Cancer. 2014;45(2):202-17.

Asch MJ, Cohen AH, Moore TC. Hepatic and splenic lymphangiomatosis with skeletal involvement: report of a case and review of the literature. Surgery. 1974;76(2):334–9.

Zhang YZ, Ye YS, Tian L, Li W. Rare case of a solitary huge hepatic cystic lymphangioma. World J Clin Cases. 2013;1(4):152–4.

Losanoff JE, Richman BW, El-Sherif A, Rider KD, Jones JW. Mesenteric cystic lymphangioma. J Am Coll Surg. 2003;196(4):598–603.

Gümüştaş OG, Sanal M, Güner O, Tümay V. Retroperitoneal cystic lymphangioma: a diagnostic and surgical challenge. Case Rep Pediatr. 2013;2013:292053.

Koh CC, Sheu JC. Hepatic lymphangioma: a case report. Pediatr Surg Int. 2000;16(7):515–6.

Enzinger FM, Weiss SW. Soft tissue tumours. 2nd edn. St Louis: CV Mosby Company; 1988: 614–637.

Ishikawa H, Uchida S, Yokokura Y, Iwasaki Y, Horiuchi H, Hiraki M, et al. Nonparasitic solitary huge liver cysts causing intracystic hemorrhage or obstructive jaundice. J Hepatobiliary Pancreatic Surg. 2002;9:764–8.

Ayyappan AP, Jhaveri KS, Haider MA. Radiological assessment of mesenteric and retroperitoneal cysts in adults: is there a role for chemical shift MRI? Clin Imaging. 2011;35(2):127–32.