Agenesis of dorsal pancreas causing extra hepatic portal vein obstruction in a patient of symptomatic cholelithiasis: a case report

Authors

  • Vipan Kumar Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
  • Niraj Gupta Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
  • Mohd Muzammil Ambekar Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
  • Neeraj Sharma Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
  • Prateek Sood Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
  • Vikrant Sharma Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
  • Narvir Singh Chauhan Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
  • Rajkumar Sharma Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India
  • Somraj Mahajan Department of Surgery, Dr. Rajendra Prasad Government Medical College, Tanda, Kangra, Himachal Pradesh, India

DOI:

https://doi.org/10.18203/2349-2902.isj20182799

Keywords:

ADP, Agenesis of dorsal pancreas, EHPVO

Abstract

Agenesis of dorsal pancreas (ADP) is an extremely rare entity. We report a case of 50 year old lady with complete agenesis of the dorsal pancreas presenting with extra-hepatic portal vein obstruction (EHPVO) with symptomatic gall stone disease. Contrast enhanced computed tomography (CECT) revealed a normal pancreatic head, but pancreatic body and tail were not visualized, pancreatic head was compressing upon the portal vein with marked luminal narrowing and cavernoma formation. Magnetic resonance imaging (MRI) and magnetic resonance cholangio pancreatography (MRCP) findings confirmed the CT findings of ADP.

References

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Fukuoka K, Ajiki T, Yamamoto M, Fujiwara H, Onoyama H, Fujita T, Katayama N, Mizuguchi K, Ikuta H, Kuroda Y, Hanioka K. Complete agenesis of the dorsal pancreas. J Hepatobiliary Pancreat Surg 1999; 6: 94-97

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Published

2018-06-25

Issue

Section

Case Reports