Rare case of symptomatic (painful) fibrous dysplasia of 12th Rib

Authors

  • Jeevan Kumar Sharma Department of Orthopaedic Surgery, B. P. Koirala Institute of Health Sciences, Dharan, Sunsari, Nepal
  • Pashupati Chaudhary Department of Orthopaedic Surgery, B. P. Koirala Institute of Health Sciences, Dharan, Sunsari, Nepal
  • Janak Das Department of Orthopaedic Surgery, Bijayapur Hospital Pvt Ltd, Dharan, Sunsari, Nepal

DOI:

https://doi.org/10.18203/2349-2902.isj20180960

Keywords:

12th Rib, Fibrous dysplasia (FD), Painful, Rare

Abstract

Fibrous dysplasia (FD) is a common benign intra- medullary lesion of the skeleton characterized by proliferation of fibro-osseous tissue. It is viewed as a developmental abnormality that is typically seen in adolescents and young adults. It can present as monostotic (70% to 80%), polyostotic fibrous dysplasia (20% to 30%), McCune-Albright syndrome (2% to 3%), or Mazabraud’s syndrome. Monostotic fibrous dysplasia accounts upto 30% in the ribs. It is often asymptomatic and incidentally detected on radiographs. We report a case of a 35-year-old lady who presented with swelling on the right chest wall of 5-year duration and was increasing in size and painful for 8 months. Her chest radiograph showed a cystic mass of the 12th rib. On computed tomography scan, mass turned out to be focal lytic lesion of the 12th rib. Surgical resection of 12th rib was done. Histopathology of the lesion confirmed the diagnosis of FD. Although it is fairly common in ribs, no previous literatures on FD of 12th rib was found. 

References

Khanna V, Shori A. Polyostotic Fibrous Dysplasia: A Case Report. Juniper Online J Case Stud. 2017;3(1):1-4.

Batista KT, Araujo HJ de, Schwartzman UPY. Monostotic fibrous dysplasia of the metacarpal: a case report. Rev Bras Ortop. 2016;51(6):730-4.

Mlika M, Boudaya S, Chermiti F. Costal Fibrous Dysplasia: A Proposal of a Managing Diagram based on a Review of the Literature. Austin J Cancer Cliical Res. 2015;2:1-4.

Ahmad Z, Zubair I. Fibrous dysplasia of rib presenting as a cystic mass in the lung. Oxford Med Case Reports. 2015;2015(2):196-9.

Ruggieri P, Sim FH, Bond JR, Krishnan Unni K. osteosarcoma in a patient with polyostotic fibrous dysplasia and albright syndrome. Mayo clinic tumour rounds. 1995;18:71-5.

Singer FR. Fibrous dysplasia of bone: the bone lesion unmasked. Am J Pathol. 1997;151(6):1511-5.

Henry A. Monostotic fibrous dysplasia. JBJS. 1969;51B(2):300-6.

DiCaprio MR, Enneking WF. Fibrous dysplasia: Pathophysiology, evaluation, and treatment. Vol. 87, Journal of Bone and Joint Surgery - Series A. 2005;87:1848-64.

Lee JW, Kim JH, Han SH, Kang HI. Fibrous Dysplasia with Aneurysmal Bone Cyst. J Korean Neurosurg Soc. 2010;48:551-4.

Fitzpatrick KA, Taljanovic MS, Speer DP, Graham AR, Jacobson JA, Barnes GR, et al. Imaging findings of fibrous dysplasia with histopathologic and intraoperative correlation. Am J Roentgenol. 2004;182(6):1389-98.

Kransdorf MJ, Moser RP, Gilkey FW. Fibrous dysplasia. Radiographics. 1990;10(3):519-37.

Mahadevappa A, Patel S, Ravishankar S, Manjunath G V. Case Report Monostotic Fibrous Dysplasia of the Rib: A Case Report. Hindawi Publ Corp Case Reports Orthop. 2012;2012:2-6.

Parekh SG, Donthineni-Rao R, Ricchetti E, Lackman RD. Fibrous dysplasia. J Am Acad Orthop Surg. 2004;12(5):305-13.

Stanton RP. Surgery for fibrous dysplasia. J Bone Miner Res. 2006;21:105-9.

Traibi A, El Oueriachi F, El Hammoumi M, Al Bouzidi A, Kabiri EH. Monostotic fibrous dysplasia of the ribs. Interact Cardiovasc Thorac Surg. 2012;14(1):41-3.

Downloads

Published

2018-03-23

Issue

Section

Case Reports